Annals of African Medicine

CASE REPORT
Year
: 2016  |  Volume : 15  |  Issue : 4  |  Page : 200--203

Dystonia, myoclonus, and encephalopathy in a single patient: A rare association of moyamoya


Ujjawal Roy1, Urmila Das1, Ajay Panwar2, Prabhat Kumar Lal3 
1 Department of Neurology, Bangur Institute of Neurosciences, IPGMER, Kolkata, West Bengal, India
2 Department of Neurology, King George's Medical University, Lucknow, Uttar Pradesh, India
3 Department of Community Medicine, Darbhanga Medical College, Laheriasarai, Bihar, India

Correspondence Address:
Ujjawal Roy
Department of Neurology, Bangur Institute of Neurosciences, IPGMER, Kolkata, West Bengal
India

Moyamoya disease (MMD) is a rare neurovascular disorder which pathologically, is a chronic cerebrovasculopathy. It is characterized by stenosis of the internal carotid artery (ICA) and the main branches within the circle of Willis with consecutive development of collateral vessels. There are a few cases in the literature which have described movement disorders as a manifestation of MMD; however these have been uncommonly reported in cases of moyamoya syndrome (MMS). We present a 10-year-old boy with dystonia, myoclonus and encephalopathy like features. These features in association with moyamoya, are rarely described.


How to cite this article:
Roy U, Das U, Panwar A, Lal PK. Dystonia, myoclonus, and encephalopathy in a single patient: A rare association of moyamoya.Ann Afr Med 2016;15:200-203


How to cite this URL:
Roy U, Das U, Panwar A, Lal PK. Dystonia, myoclonus, and encephalopathy in a single patient: A rare association of moyamoya. Ann Afr Med [serial online] 2016 [cited 2023 Feb 9 ];15:200-203
Available from: https://www.annalsafrmed.org/article.asp?issn=1596-3519;year=2016;volume=15;issue=4;spage=200;epage=203;aulast=Roy;type=0